B. Figure, 1 -Résultats obtenus sur l'ensemble des séquences vidéos

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, Ce syndrome est marqué par une hypotonie néonatale, puis au cours du développement, apparaissent l'hyperphagie, les troubles de la satiété et des troubles comportementaux. Sur le plan social, ces patients ont des interactions sociales atypiques, en France dont les deux origines génétiques les plus fréquentes sont la délétion de la région 15q11q12 du chromosome 15 paternel et la disomie maternelle

S. Dans-le, les données concernant les troubles du comportement et les troubles des interactions sociales sont rares. Il est détaillé que ces patients ont des déficits de reconnaissance des émotions et des signatures cérébrales en réponse aux visages atypiques. Néanmoins, beaucoup de processus de traitement des signaux sociaux restent encore inexplorés

, Nous avons démontré que les patients avec un SPW avaient une lenteur motrice et perceptive. De plus, nous relevons un déficit de traitement des visages, mais qui n'est pas généralisable aux voix. Selon nous, les déficits présents sur le traitement des visages, pourraient provenir d'un trouble dans la perception globale et dans l'unification de plusieurs sources d'informations entreelles, faisant référence à la cohérence centrale. Enfin, nous avons montré que globalement, les patients avec une disomie souffrent de troubles sociaux plus sévères que les patients avec une délétion. Par ailleurs, un versant thérapeutique est développé avec l'administration d'ocytocine (OT) chez les enfants et les adultes avec un SPW. L'OT a, au cours des dernières années, fait l'objet d'un vif intérêt pour les populations ayant des troubles des interactions sociales. Ce versant thérapeutique permettra d, Cette thèse permet d'apporter de nouvelles données sur les processus de traitement des voix et des visages qui pourraient être altérés dans le SPW