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Acquisition de la lecture chez les personnes porteuses du syndrome de Williams

Abstract : Williams syndrome (WS) is a rare genetic disease involving an intellectual developmental disorder (ID). Regarding the neuropsychological level, a consensus around a dissociation profile between relatively preserved oral language and other impaired cognitive abilities is reported in the literature. Despite these specificities, few studies have investigated the learning aspects in this population, and more specifically the reading area. Three explanatory hypotheses are shared by the few reported results regarding the reading acquisition difficulties: intellectual efficiency, metaphonological abilities and, more recently, visuospatial processing. In line with this work, our research attempts, for the first time in France, to better understand the reading difficulties acquisition by people with the WS. Our two objectives were to characterize the reading procedures and to identify the skills involved in the installation of written words identification. Our first two studies present an inventory of the curent research about people with ID and WS. Beyond the level of intellectual efficiency, our observations indicate that these people have reading skills despite the deficits in certain cognitive skills. Our last three articles explain the exploratory results of our two studies, transversal and longitudinal, using standardized tests and matching chronological age, mental age, vocabulary level and reading level. The results demonstrate an involvement of metaphonological and visuospatial skills, respectively, in setting up the sublexical procedure and the orthographic recovery of written words. Finally, we are discussed about therapeutic and remediation treatment that can be appropriate to our study population, but more broadly, to other atypical populations.
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Submitted on : Tuesday, October 2, 2018 - 3:40:06 PM
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  • HAL Id : tel-01886109, version 1


Anne-Sophie Pezzino. Acquisition de la lecture chez les personnes porteuses du syndrome de Williams. Psychologie. Université Rennes 2, 2018. Français. ⟨NNT : 2018REN20033⟩. ⟨tel-01886109⟩



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